Demographic and clinical parameters during acute phase of the pediatric cohort study (n = 70)
| Parameters | Median (25th–75th percentile) or number of patients (percentage) |
|---|---|
| Age (years old), n = 70 | 6.5 (2–12) |
| Sex—male, n = 70 | 36 (51%) |
| Hemoglobin (g/dL), n = 58 | 8.2 (6.5–9.9) |
| Hematocrit (%), n = 60 | 23 (19–30) |
| Platelets (× 109/L), n = 59 | 51 (28–80) |
| LDH (IU/L), n = 55 | 2,670 (1,366–4,422) |
| Urea (mg/dL), n = 56 | 132 (80–172) |
| Creatinine (mg/dL), n = 56 | 2.60 (1.37–6.08) |
| Complement genetic testing completed | |
| MLPA | 12 (17%) |
| Sanger or NGS | 14 (20%) |
| Anti-FH autoantibodies testing | |
| Positive | 14 (20%) |
| Negative | 56 (80%) |