Thresholds for elective surgical intervention prior to pregnancy and indication for caesarean section [35]
Disease | Indication prepregnant surgery | Indication caesarean section |
---|---|---|
Marfan syndrome | ≥ 45 mm | ≥ 45 mm |
Turner syndrome | ≥ 27 mm/m2 | ≥ 27 mm/m2 |
Bicuspid aortic valve | ≥ 50 mm | ≥ 45 mm |
Loeys-Dietz syndrome | ≥ 45 mm | ≥ 45 mm |
Vascular Ehlers-Danlos Syndrome | Contraindicated | Always |
Others | ≥ 50 mm | ≥ 45 mm |